comida-PKU Concept

The dietary management consists of a diet low in phenylalanine (i.e. low in native protein) with addition of amino acids supplements free from phenylalanine.

Background:
Phenylketonuria is an inherited rare disorder in metabolism of the amino acid phenylalanine. Individuals with PKU have a defect of the enzyme phenylalanine hydroxylase, which is responsible for the degradation of the amino acid phenylalanine. The consequence is an accumulation of phenylalanine and its metabolites in the body, which is toxic to the central nervous system. If not treated, this condition results in brain damages and mental retardation.

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COMIDAMED

Dr. Schär Deutschland GmbH 


Dieselstrasse 23
61191 Rosbach v. d. H. · DE


Tel. +49 6003 9117 23
Hotline DE: 0800 153 153-3
Hotline AT: 0800 500 144
info@comidamed.de

 

 

COMIDACLOUD

Aminosäurenmischung | diätetische Behandlung von Phenylketonurie | erstes Lebensjahr | Erwachsene | glutenfrei | HPA | Hyperphenylalaninämie | Jugendliche | Kinder | Kleinkinder | Kohlenhydrate | Mineralstoffe | phenylalaninfreie | Proteinsupplemente | Phenylketonurie | PKU | Schwangere |Spurenelemente | Säuglinge | Vitamine

COMIDATAGS

Germany | Entwicklung | Herstellung | spezielle Ernährung | medizinisch | Nährstoffe | Rosbach |