The dietary management consists of a diet low in phenylalanine (i.e. low in native protein) with addition of amino acids supplements free from phenylalanine.
Phenylketonuria (PKU)
Background:
Phenylketonuria is an inherited rare disorder in metabolism of the amino acid phenylalanine. Individuals with PKU have a defect of the enzyme phenylalanine hydroxylase, which is responsible for the degradation of the amino acid phenylalanine. The consequence is an accumulation of phenylalanine and its metabolites in the body, which is toxic to the central nervous system. If not treated, this condition results in brain damages and mental retardation.
PDF data sheet
comida-PKU A formula is for infants in their first year of life.
comida-PKU A formula consists of a special infant formula free from Phenylalanine, containing LCP and carbohydrates according to standard infant formulas.
(EU Infant Formula Directive; SCF; DRI).
comida-PKU A formula data sheet
comida-PKU A is for infants in their first year of life.
comida-PKU A consists of a concentrated amino acid mixture free from Phenylalanine and fat, supplemented with micronutrients according to current international recommended dietary intakes for infants.
(DACH; SCF; DRI).
comida-PKU A data sheet
comida-PKU B formula is for is for toddlers and children between 1 and 14 years.
comida-PKU B formula consists of a special formula free from Phenylalanine, containing omega-3, omega-6 fatty acids and carbohydrates according to current international recommended dietary intakes for children
(DACH; SCF; DRI).
comida-PKU B formula data sheet
comida-PKU B is for toddlers and children between 1 and 14 years.
comida-PKU B consists of a concentrated amino acid mixture free from Phenylalanine and fat, supplemented with micronutrients according to current international recommended dietary intakes for children
(DACH; SCF; DRI).
comida-PKU B formula data sheet
comida-PKU C is for children adults and pregnants at ages over 15 years.
comida-PKU C consists of a highly concentrated amino acid mixture free from Phenylalanine and fat, supplemented with micronutrients according to current international recommended dietary intakes for children
(DACH; SCF; DRI).
comida-PKU C data sheet
comida-PKU B formula cream ORANGE-Lemon is for is for toddlers and children between 1 and 14 years.
comida-PKU B formula cream ORANGE-Lemon consists of a special formula free from Phenylalanine, containing omega-3, omega-6 fatty acids and carbohydrates according to current international recommended dietary intakes for children
(DACH; SCF; DRI).
comida-PKU B formula cream ORANGE-Lemon data sheet
comida-PKU C formula is for children adults and pregnants at ages over 15 years.
comida-PKU C formula consists of a concentrated amino acid mixture free from Phenylalanine and fat, supplemented with micronutrients according to current international recommended dietary intakes for children
(DACH; SCF; DRI).
comida-PKU C formula data sheet
comida-PKU C formula Fresh ORANGE-Lemon is for children adults and pregnants at ages over 15 years.
comida-PKU C formula Fresh ORANGE-Lemon consists of a concentrated amino acid mixture free from Phenylalanine and fat, supplemented with micronutrients according to current international recommended dietary intakes for children
(DACH; SCF; DRI).
comida-PKU C formula Fresh ORANGE-Lemon data sheet
comida-PKU C capsules are for children, adults and pregnants at ages over 15 years.
comida-PKU C capsules consist of a highly concentrated amino acid mixture free from Phenylalanine and fat, supplemented with micronutrients according to current international recommended dietary intakes for children
(DACH; SCF; DRI).
comida-PKU C capsules data sheet
